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Gene Ontology Information

Protein Name Mia40p
Description Import and assembly protein in mitochondrial intermembrane space; component of MIA pathway which mediates import and oxidative folding of substrates including small proteins containing twin cysteine motifs; acts in concert with Erv1p, which oxidizes the cysteine residues of Mia40p to comprise a disulfide relay system that catalyzes import; also mediates folding of Atp23p via a chaperone-like activity; forms a dimer that binds iron-sulfur cluster in vitro
GO Terms:
Biological Process
level 3: protein folding external link
level 4: protein maturation by protein folding external link
level 5: protein import into mitochondrial intermembrane space external link
level 5: protein transport external link
GO Terms:
Molecular Function
level 3: oxidoreductase activity external link
level 4: protein-disulfide reductase activity external link
level 4: protein disulfide isomerase activity external link
level 5: 2 iron, 2 sulfur cluster binding external link
level 6: thiol oxidase activity external link
GO Terms:
Cellular Component
level 3: membrane external link
level 4: integral component of membrane external link
level 4: mitochondrion external link
level 6: mitochondrial inner membrane external link
level 6: mitochondrial intermembrane space external link
level 7: integral component of mitochondrial inner membrane external link
External source Open in SGD external link
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